EGPA-associated nasal polyposis should be managed with medically (ie, biologics, anti-inflammatory drugs, and topical corticosteroids) and, in some cases, surgery. Nasal polyposis associated with ...

Patients with GPP who experienced flares had higher hospitalization rates (12.2% vs 6.9%) compared to those who did not flare. Patients with generalized pustular psoriasis (GPP) who experience flares ...

About 61% of patients with ATTR-PN had at least 2 comorbidities. Patients with transthyretin amyloid polyneuropathy (ATTR-PN) have a high rate of comorbidities and substantial direct healthcare and ...

Women who desire to become pregnant should be counseled on the significance of alloimmunization as a substantial risk during pregnancy. A pregnant woman with hemolytic disease of the fetus and newborn ...

The rapid onset and resolution of the pustular eruption upon discontinuation of isotretinoin further supported the diagnosis of AGEP. Isotretinoin has the potential to trigger acute generalized ...

Although a biopsy is essential to diagnose IgG4-RD and AAV, in those cases in which a biopsy cannot be performed, clinical features and supportive imaging or laboratory data may provide important ...

In diagnosed cases of cutaneous mastocytosis, investigations to rule out systemic mastocytosis may be appropriate. A young child with a small chest lump and anemia was found to have cutaneous ...

Although no patients presented with severe disease, GPP still imposed a substantial burden on quality of life. Associations between therapies and quality of life (QoL) scores differ substantially in ...

Castleman disease and IgG4-RD have overlapping disease manifestations that can complicate the diagnostic process. A male patient initially suspected of having immunoglobulin G4-related disease ...

Pregnancies affected by multiple alloantibodies had significantly higher antibody titers and an increased need for intrauterine transfusion. Pregnancies complicated by multiple alloantibodies rather ...

Detecting synchronous or discordant lymphomas that arise in different anatomical areas is only possible by collecting samples from several sites. A 60-year-old female patient presented with a rare ...

Autopsy results showed the patient had had previous seizure activity in the brain and cellular interstitial thickening in the lungs. Sudden unexpected death in epilepsy (SUDEP), sudden death in viral ...